KINDERRADIOLOGIE ONLINE - view radiology images and radiology cases
Lesen Sie diese Seite auf Deutsch   Read this page in English
The Peer Reviewed Pediatric Radiology Platform on the Web
ISSN: 1942-955X :: Publisher: EduRad ::Editor-In-Chief: Roland Talanow, MD, PhD  
Browse Browse || Search Search || Online Book Systematically Online Book Systematically || Discussion Forum Discussion Forum || News News || Submit a Case Submit a Case || Rules Rules |
Most Interesting Cases Most Interesting Cases || "Most Diligent" Authors "Most Diligent" Authors || Case of the Day Case of the Day || Teaching files Teaching files || Links Links |
Newsletter Newsletter || Start Start || Survey Survey || Your Opinion Your Opinion || My Profile My Profile || CME-Credits CME-Credits |
    Pediatric Radiology News / Ads / Jobs Get the Pediatric Radiology News as RSS feed !
    Send us your news or ads for free
  • CME Kurs: Paediatric Body MRI

  • CME course: Paediatric Body MRI

  • Universitätsklinikum Jena sucht eine Ärztin/einen Arzt in Weiterbildung in Vollzeit

  • Kinderspital Zürich sucht Oberärztin / Oberarzt (100 %)

  • Kinderradiologische Oberärztin / Oberarzt gesucht

  • 2 Stellen in der Kinderradiologie - 1 Assistenzärztin/Assistenzarzt und 1 Oberärztin/Oberarzt in Voll- oder Teilzeit

  • Senior Paediatric Radiologist in Pediatric Radiology section needed

  • Facharzt als Oberärztin / Oberarzt in Sektion Kinderradiologie gesucht

  • Stellenangebot für Assistenzarzt (m/w) zur Facharztausbildung für RADIOLOGIE und/oder KINDERRADIOLOGIE

  • „Fellow“-Stelle zur Weiterbildung in Pädiatrischer Radiologie am Kinderspital Zürich

  • Fellow-Stelle Pädiatrische Neuroradiologie

  • FFF Kinderradiologie - Muskuloskelettale Radiologie im Kindesalter (Fit für den Facharzt)

  • Assistenzarzt für Kinderradiologe gesucht an Universitätsklinikum Schleswig-Holstein, Campus Kiel

  • Turnusarzt (m/w) in Ausbildung zum Facharzt (m/w) für Radiologie

  • Assistenzarzt (m/w) zur Weiterbildung im Schwerpunkt Kinderradiologie

  • Send us your news or ads for free

    Get the Pediatric Radiology News as RSS feed !


    The dynamic Radiology community for education, research and practice


    Case of the Day
    Angiomyolipomas of the kidney in Bourneville-Pringle's disease

    Modality: Ultrasound Modality: Ultrasound Modality: MRI Modality: MRI

    View here all images of this case in different sizes !

    Go to the top of the page ID: 20011129180447
    | The authors | Discussion | Write comments about this Case |
    | Recommend this Case to a Colleague |
     Angiomyolipomas of the kidney in Bourneville-Pringle's disease   
     Available images: There are Ultrasound images available for this case. [ Ultrasound ] There are Ultrasound images available for this case. [ MRI ]   

    Wolfgang Hirsch, Carsten Bock (Halle)  

     Email Address:

    Viewable for logged on visitors (Log on)  






    The kidney changes are mostly likely found in the course of a tuberous cerebral sclerosis (Bourneville-Pringle's disease: Skin, cerebral and pulmonary changes). Sometimes also seen as a chance finding in kidney sonography (as first directing finding of a tuberous cerebral sclerosis). Very rare are kidney symptoms (i.e. Hematuria, palpable tumor).  

     Pathomorphology or Pathophysiology of this disease :

    Composition of different parts of vessels, muscles and fat tissue. The presenting symptoms therefore vary in accordance to the composition of these tissues.

    A single angiomyolipoma must not be indicative for Bourneville - Pringle's Disease.

    See also:
    Tuberous cerebral sclerosis;


     Radiological findings:

    Ultrasound 1 <- view Ultrasound 1

    Ultrasound 1: Multiple, echo rich small tumors. Also frequently associated with multiple cysts.

    Ultrasound 2 <- view Ultrasound 2

    Ultrasound 2: Multiple, echo rich small tumors.

    MRI 1 <- view MRI 1

    MRT 1: (Coronal - FLASH 2D sequence with fat supression)

    MRI 2 <- view MRI 2

    MRT 2: (Transversal - FLASH 2D sequence with fat supression)

    Hyperintense in T1 and T2, due to the high fat content. Often obvious enhancement (only in ares of high vasculature). Frequently well-seen in fat-reducing sequences.
    CT: fat equivalent (i.e. negative HU-values in CT), occasionally however also denser representation (in higher vasculature or muscle).


     Diagnosis confirmation:

    Total constellation (Consens)  

     Which DD would be also possible with the radiological findings:

    If cystic parts predominate: polycystic kidney disease

    Teratoma (otherwise difficult differentials, particularly if hemorrhaging changes the picture); angiomyelofibromas do not calcify, in contrast to teratomas.

     Course / Prognosis / Frequency / Other :


     Comments of the author about the case:


     First description / History:






     Most likely etiology:


     Available images: There are Ultrasound images available for this case. [ Ultrasound ] There are Ultrasound images available for this case. [ MRI ]   
    More cases from these authors: Search Wolfgang Hirsch in Medline Wolfgang Hirsch (17)   Search Wolfgang Hirsch in Medline Carsten Bock (9)     

    Discussion >> Write Comment <<

      There are no comments available regarding this case.

     Write a comment to this case (With * marked fields have to be filled)

    Type in this number: 8219

    Name: *



    Subject: *

    Text: *

      Pediatric Radiology Discussion Get the Pediatric Radiology Discussion as RSS feed !
      To the discussion forum
      To the discussion forum

      Get the Pediatric Radiology Discussion as RSS feed !

      © 2001-2020
      In cooperation with © Radiolopolis - Radiology Search - Radiology Teacher - PubMed Reader - Annotate - Radiology Lectures & Tutorials - Radiology Boards Preparation - Pediatric Radiology Links - Pediatric Radiology Information - Emergency Radiology - Lung Cancers - USMLE Forums - Cancer Staging Information - Chest Radiology - Radiology Case Report Journal
      For suggestions and questions:
      Add this site to your favorites (CTRL+D)