KINDERRADIOLOGIE ONLINE - view radiology images and radiology cases
Lesen Sie diese Seite auf Deutsch   Read this page in English
The Peer Reviewed Pediatric Radiology Platform on the Web
ISSN: 1942-955X :: Publisher: EduRad ::Editor-In-Chief: Roland Talanow, MD, PhD  
Browse Browse || Search Search || Online Book Systematically Online Book Systematically || Discussion Forum Discussion Forum || News News || Submit a Case Submit a Case || Rules Rules |
Most Interesting Cases Most Interesting Cases || "Most Diligent" Authors "Most Diligent" Authors || Case of the Day Case of the Day || Teaching files Teaching files || Links Links |
Newsletter Newsletter || Start Start || Survey Survey || Your Opinion Your Opinion || My Profile My Profile || CME-Credits CME-Credits |
    Pediatric Radiology News / Ads / Jobs Get the Pediatric Radiology News as RSS feed !
    Send us your news or ads for free
  • Dual-energy compared to single-energy CT in pediatric imaging: a phantom study for DECT clinical gui... (Pediatr Radiol)
  • Echocardiography and Focused Cardiac Ultrasound.... (Pediatr Crit Care Med)
  • Prognostic and Predictive Values of Diffusion and Perfusion MRI in Pediatric Intracranial Ependymoma... (Br J Radiol)
  • CME Kurs: Paediatric Body MRI

  • CME course: Paediatric Body MRI

  • Universitätsklinikum Jena sucht eine Ärztin/einen Arzt in Weiterbildung in Vollzeit

  • Kinderspital Zürich sucht Oberärztin / Oberarzt (100 %)

  • Kinderradiologische Oberärztin / Oberarzt gesucht

  • 2 Stellen in der Kinderradiologie - 1 Assistenzärztin/Assistenzarzt und 1 Oberärztin/Oberarzt in Voll- oder Teilzeit

  • Senior Paediatric Radiologist in Pediatric Radiology section needed

  • Facharzt als Oberärztin / Oberarzt in Sektion Kinderradiologie gesucht

  • Stellenangebot für Assistenzarzt (m/w) zur Facharztausbildung für RADIOLOGIE und/oder KINDERRADIOLOGIE

  • „Fellow“-Stelle zur Weiterbildung in Pädiatrischer Radiologie am Kinderspital Zürich

  • Fellow-Stelle Pädiatrische Neuroradiologie

  • FFF Kinderradiologie - Muskuloskelettale Radiologie im Kindesalter (Fit für den Facharzt)

  • Assistenzarzt für Kinderradiologe gesucht an Universitätsklinikum Schleswig-Holstein, Campus Kiel

  • Turnusarzt (m/w) in Ausbildung zum Facharzt (m/w) für Radiologie

  • Assistenzarzt (m/w) zur Weiterbildung im Schwerpunkt Kinderradiologie

  • Send us your news or ads for free

    Get the Pediatric Radiology News as RSS feed !


    Radiolopolis

    The dynamic Radiology community for education, research and practice


     

    Go to the top of the page   ID: 20011218135646 Original case in english  More links about this topic on Pubmed (PubMed Reader)
    Add this case to your RSS feeder: Subscribe to RSS feed Add to Yahoo Add to Google Add to AOL Add to Furl Subscribe to Feed Burner feed

    Bookmark and Share


    | The Authors | Discussion | Write a Comment to this Case |
    | Evaluate this Case | Recommend this Case to a Colleague |
    | Citation | Similar Cases | Similar Cases in the Internet | Images to this Case |
     
    Tuberous sclerosis of the brain with hemimegalencephaly
    G Hahn. Tuberous sclerosis of the brain with hemimegalencephaly. PedRad [serial online] vol 1, no. 12.
    URL: www.PedRad.info/?search=20011218135646


     
     Pediatric Radiology CasesImages to this case: There are MRI-images available for this case. [ MRI ] View all modalities [ All ]   
     Pediatric Radiology CasesAuthor/s:

    G. Hahn (Dresden)  

     
     Pediatric Radiology CasesEmail Address:

    Viewable for logged on visitors (Log on)  

     
     Pediatric Radiology CasesAge:

    N/A  

     
     Pediatric Radiology CasesGender:

    N/A  

     
     Pediatric Radiology CasesRegion-Organ:

    Head-Brain and brain nerves  

     
     Pediatric Radiology CasesMost likely etiology:

    congenital  

     
     Pediatric Radiology CasesHistory:

    After normal pregnancy and birth in the 39th gestational week, the patient was admitted due to infection. Seizures were observed. Additionally, a 2/6 systolicum was noticed. No skin changes were seen. In sonographic examination, 20 to 21 mm, echogenic rhabdomyomas were seen, which, however, were asymptomatic, and did not change in size.  

     
     Pediatric Radiology CasesPathomorphology or Pathophysiology of this disease :

    The name, "Hemimegalencephaly," is used to describe a hamartous enlargening of one or of parts of the hemisphere. It is associated with defects in the neuronal proliferation, migration and organization. The many different radiological and pathological depictions allow to assume that hemimegalencephaly is heterogenic and includes many different illnesses. The brain can be afflicted by itself, or it can be associated with a hemihypertrophy of the complete (or parts) of the ipsilateral side.  

     
     Pediatric Radiology CasesRadiological findings:


    MRI 1 <- view MRI 1

    MRI 1: Skull image (T1-weighted Sequence after contrast): Partial Hemimegalencephaly on the left side of tuberous brain sclerosis. Large left hemisphere with large left lateral ventricle. Thickened, atypically gyrated cortex and subcortical dismyelination (increased signal). In the Foramen of Monro on the right, subependymal nodule and also on the right, subcortical tuberoma.





    MRI 2 <- view MRI 2

    MRI 2: Skull image (T2-weighted Sequence): Partial Hemimegalencephaly on the left side of tuberous brain sclerosis. Large left hemisphere with large left lateral ventricle. Thickened, atypically gyrated cortex and subcortical dismyelination (decreased signal).


     

     
     Pediatric Radiology CasesDiagnosis confirmation:

    Total constellation (Consens)  

     
     Pediatric Radiology CasesWhich DD would be also possible with the radiological findings:

    Hemimegalencephaly due to other illnesses: Proteus-syndrome, epidermal naevus syndrome, hypomelanosis Ito, Neurofibromatosis Type I  

     
     Pediatric Radiology CasesCourse / Prognosis / Frequency / Other :

    Often, this develops into hard-to-treat seziures or seizures that are difficult to control by medication. Therefore, a surgical procedure is often performed.  

     
     Pediatric Radiology CasesComments of the author about the case:

    N/A  

     
     Pediatric Radiology CasesFirst description / History:

    Hemimegalencephaly was first described in 1835.  

     
     Pediatric Radiology CasesLiterature:

    N/A  

     
     Pediatric Radiology CasesKeywords:

    Hemimegalencephaly, Epilepsy, seizures, systolicum, heart murmur, rhabdomyoma, hamartous enlargening of the brain, tuberous sclerosis of the brain, child, childhood, pediatric radiology  

     
     Pediatric Radiology Cases Cite this article:

    G Hahn. Tuberous sclerosis of the brain with hemimegalencephaly. PedRad [serial online] vol 1, no. 12.
    URL: www.PedRad.info/?search=20011218135646  

     
     Pediatric Radiology Cases Read similar articles: with corresponding keywords
    in the same field: Head-Brain and brain nerves
    or in the region: Head
    or in the tissue/organ: Brain and brain nerves
    or with the etiology: congenital
     
     Pediatric Radiology CasesImages to this case: There are MRI-images available for this case. [ MRI ] View all modalities [ All ]   
     
    Tuberous sclerosis of the brain with hemimegalencephaly
    G Hahn. Tuberous sclerosis of the brain with hemimegalencephaly. PedRad [serial online] vol 1, no. 12.
    URL: www.PedRad.info/?search=20011218135646


     

    Search similar cases in:
    More links about this topic on Pubmed  More links about this topic on Yahoo  More links about this topic on Altavista  More links about this topic on MSN  More links about this topic on Google  More links about this topic on Fireball

    Peer-reviewed Radiology Search



    Tuberous sclerosis of the brain with hemimegalencephaly
    Other cases by these authors:

    Search G. Hahn in Medline G. Hahn (22)   

    Tuberous sclerosis of the brain with hemimegalencephaly  
     
    Tuberous sclerosis of the brain with hemimegalencephaly
    G Hahn. Tuberous sclerosis of the brain with hemimegalencephaly. PedRad [serial online] vol 1, no. 12.
    URL: www.PedRad.info/?search=20011218135646


     
     
    Tuberous sclerosis of the brain with hemimegalencephaly
    G Hahn. Tuberous sclerosis of the brain with hemimegalencephaly. PedRad [serial online] vol 1, no. 12.
    URL: www.PedRad.info/?search=20011218135646


     

    Medical Dictionary
    Search in medical dictionary for
    Or type in a keyword
    ( Provided by The On-Line Medical Dictionary )




    How interesting was this case for you?
    (10 = most interesting || 1 = less interesting)
     
    Tuberous sclerosis of the brain with hemimegalencephaly
    G Hahn. Tuberous sclerosis of the brain with hemimegalencephaly. PedRad [serial online] vol 1, no. 12.
    URL: www.PedRad.info/?search=20011218135646


     




    Discussion >> Write Comment <<



      There are no comments available regarding this case.





     Write a comment to this case (With * marked fields have to be filled)

    Type in this number: 2147

    Name: *

    E-Mail:

    Website:

    Subject: *

    Text: *




     
      Pediatric Radiology Discussion Get the Pediatric Radiology Discussion as RSS feed !
      To the discussion forum
      To the discussion forum

      Get the Pediatric Radiology Discussion as RSS feed !

      © 2001-2016   www.kinderradiologie-online.de
      In cooperation with © Radiolopolis - Radiology Search - Radiology Teacher - PubMed Reader - Annotate - Radiology Lectures & Tutorials - Radiology Boards Preparation - Pediatric Radiology Links - Pediatric Radiology Information - Emergency Radiology - Lung Cancers - USMLE Forums - Cancer Staging Information - Chest Radiology - Radiology Case Report Journal
      For suggestions and questions: information@kinderradiologie-online.de
      Add this site to your favorites (CTRL+D)