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    Go to the top of the page   ID: 20011129180447 Original case in english  More links about this topic on Pubmed (PubMed Reader)
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    Angiomyolipomas of the kidney in Bourneville-Pringle's disease
    Wolfgang Hirsch, Carsten Bock. Angiomyolipomas of the kidney in Bourneville-Pringle's disease. PedRad [serial online] vol 1, no. 11.
    URL: www.PedRad.info/?search=20011129180447


    ( There are questions in the CMK-Mode for this topic )

     
     Pediatric Radiology CasesImages to this case: There are Ultrasound-images available for this case. [ Ultrasound ] There are MRI-images available for this case. [ MRI ] View all modalities [ All ]   
     Pediatric Radiology CasesAuthor/s:

    Wolfgang Hirsch, Carsten Bock (Halle)  

     
     Pediatric Radiology CasesEmail Address:

    Viewable for logged on visitors (Log on)  

     
     Pediatric Radiology CasesAge:

    N/A  

     
     Pediatric Radiology CasesGender:

    N/A  

     
     Pediatric Radiology CasesRegion-Organ:

    Abdomen-Renals  

     
     Pediatric Radiology CasesMost likely etiology:

    neoplastic  

     
     Pediatric Radiology CasesHistory:

    The kidney changes are mostly likely found in the course of a tuberous cerebral sclerosis (Bourneville-Pringle's disease: Skin, cerebral and pulmonary changes). Sometimes also seen as a chance finding in kidney sonography (as first directing finding of a tuberous cerebral sclerosis). Very rare are kidney symptoms (i.e. Hematuria, palpable tumor).  

     
     Pediatric Radiology CasesPathomorphology or Pathophysiology of this disease :

    Composition of different parts of vessels, muscles and fat tissue. The presenting symptoms therefore vary in accordance to the composition of these tissues.

    A single angiomyolipoma must not be indicative for Bourneville - Pringle's Disease.

    See also:
    Tuberous cerebral sclerosis;
    Lymphangioleiomyomatosis.

     

     
     Pediatric Radiology CasesRadiological findings:


    Ultrasound 1 <- view Ultrasound 1

    Ultrasound 1: Multiple, echo rich small tumors. Also frequently associated with multiple cysts.



    Ultrasound 2 <- view Ultrasound 2

    Ultrasound 2: Multiple, echo rich small tumors.



    MRI 1 <- view MRI 1

    MRT 1: (Coronal - FLASH 2D sequence with fat supression)



    MRI 2 <- view MRI 2

    MRT 2: (Transversal - FLASH 2D sequence with fat supression)

    Hyperintense in T1 and T2, due to the high fat content. Often obvious enhancement (only in ares of high vasculature). Frequently well-seen in fat-reducing sequences.
    CT: fat equivalent (i.e. negative HU-values in CT), occasionally however also denser representation (in higher vasculature or muscle).



     

     
     Pediatric Radiology CasesDiagnosis confirmation:

    Total constellation (Consens)  

     
     Pediatric Radiology CasesWhich DD would be also possible with the radiological findings:

    If cystic parts predominate: polycystic kidney disease

    Teratoma (otherwise difficult differentials, particularly if hemorrhaging changes the picture); angiomyelofibromas do not calcify, in contrast to teratomas.
    Nephroblastomatosis  

     
     Pediatric Radiology CasesCourse / Prognosis / Frequency / Other :

    N/A  

     
     Pediatric Radiology CasesComments of the author about the case:

    N/A  

     
     Pediatric Radiology CasesFirst description / History:

    N/A  

     
     Pediatric Radiology CasesLiterature:

    N/A  

     
     Pediatric Radiology CasesKeywords:

    Angiomyolipoma, kidney, Bourneville-Pringle's disease, tuberous sclerosis of the brain, child, childhood, pediatric radiology  

     
     Pediatric Radiology Cases Cite this article:

    Wolfgang Hirsch, Carsten Bock. Angiomyolipomas of the kidney in Bourneville-Pringle's disease. PedRad [serial online] vol 1, no. 11.
    URL: www.PedRad.info/?search=20011129180447  

     
     Pediatric Radiology Cases Read similar articles: with corresponding keywords
    in the same field: Abdomen-Renals
    or in the region: Abdomen
    or in the tissue/organ: Renals
    or with the etiology: neoplastic
     
     Pediatric Radiology CasesImages to this case: There are Ultrasound-images available for this case. [ Ultrasound ] There are MRI-images available for this case. [ MRI ] View all modalities [ All ]   
     
    Angiomyolipomas of the kidney in Bourneville-Pringle's disease
    Wolfgang Hirsch, Carsten Bock. Angiomyolipomas of the kidney in Bourneville-Pringle's disease. PedRad [serial online] vol 1, no. 11.
    URL: www.PedRad.info/?search=20011129180447


    ( There are questions in the CMK-Mode for this topic )

     

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    Angiomyolipomas of the kidney in Bourneville-Pringle's disease
    Other cases by these authors:

    Search Wolfgang Hirsch in Medline Wolfgang Hirsch (17)   
    Search Carsten Bock in Medline Carsten Bock (9)   

    Angiomyolipomas of the kidney in Bourneville-Pringle's disease  
     
    Angiomyolipomas of the kidney in Bourneville-Pringle's disease
    Wolfgang Hirsch, Carsten Bock. Angiomyolipomas of the kidney in Bourneville-Pringle's disease. PedRad [serial online] vol 1, no. 11.
    URL: www.PedRad.info/?search=20011129180447


    ( There are questions in the CMK-Mode for this topic )

     
     
    Angiomyolipomas of the kidney in Bourneville-Pringle's disease
    Wolfgang Hirsch, Carsten Bock. Angiomyolipomas of the kidney in Bourneville-Pringle's disease. PedRad [serial online] vol 1, no. 11.
    URL: www.PedRad.info/?search=20011129180447


    ( There are questions in the CMK-Mode for this topic )

     

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    Angiomyolipomas of the kidney in Bourneville-Pringle's disease
    Wolfgang Hirsch, Carsten Bock. Angiomyolipomas of the kidney in Bourneville-Pringle's disease. PedRad [serial online] vol 1, no. 11.
    URL: www.PedRad.info/?search=20011129180447


    ( There are questions in the CMK-Mode for this topic )

     




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